Gall Bladder

Gall
Bladder

  

• CM
  Hollands, FJ Rivera-Pedrogo, R Gonzalez-Vallina, et al
  (Miami Children’s Hosp, Fla)  
  
  Ileal
  exclusion for Byler’s disease: An alternative surgical
  aprooach with promising early results for pruritus.  
  
  
  J Pediatr
  Surg 33:220-224, 1998.
  
       
  
  Progressive
  familial intrahepatic 
  cholestasis (PFIC) – also called Byler’s
  disease – is an uncommon cause of hepatocellular
  cholestasis.  Affected
  children have intermittent, painless jaundice.
  Intense pruritus disproportionate to the degree
  of hyperbilirubinemia can lead to self-mutilation by
  scratching. Good
  results have been achieved with liver transplantation
  and cutaneous biliary diversion procedures, both of
  which have their complications.
  Ileal exclusion or bypass procedures offer some
  important potential advantages over these approaches.